Adams–Oliver syndrome (AOS) is a rare congenital disorder defined by a distinct combination of features, including scalp and skull defects, which are classified as cutis aplasia congenita, transverse limb defects, and mottled skin. The manifestations of AOS primarily encompass two significant aspects. Firstly, aplasia cutis congenita is characterized by the absence of skin in specific areas of the body at birth, with this condition typically observed at the vertex of the skull.